From: The ESHRE–ESGE consensus on the classification of female genital tract congenital anomalies
Main class | Main sub-class | Co-existent sub-class | |
---|---|---|---|
Uterine anomaly | Cervical/vaginal anomaly | ||
Class 0 | Normal uterus | Cervix | |
C0 Normal | |||
Class I | Dysmorphic uterus | a. T-shaped | C1 Septate |
b. Infantilis | C2 Double “normal” | ||
Class II | Septate uterus | a. Partial | C3 Unilateral aplasia / dysplasia |
b. Complete | C4 Aplasia/dysplasia | ||
Class III | Dysfused uterus (including dysfused “septate”) | a. Partial | |
b. Complete | Vagina | ||
Class IV | Unilaterally formed uterus | a. Rudimentary horn with cavity (communicating or not) | V0 Normal vagina |
V1 Longitudinal non-obstructing vaginal septum | |||
b. Rudimentary horn without cavity/aplasia (no horn) | V2 Longitudinal obstructing vaginal septum | ||
Class V | Aplastic/dysplastic | a. Rudimentary horn with cavity (bi- or unilateral) | V3 Transverse vaginal septum/imperforate hymen |
b. Rudimentary horn without cavity (bi- or unilateral)/aplasia | V4 Vaginal aplasia | ||
Class VI | Unclassified malformations |